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Diabetes Insipidus¿ä¾àÁ¤¸®

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  • ÀúÀ۽ñâ : 2007/01
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¼Ò°³±Û diabetes insipidus ÇØ¸®½¼part °£´ÜÇÏ°Ô ¿ä¾àÁ¤¸®ÇÑ °ÍÀÔ´Ï´Ù.
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AVPºÐºñ ȤÀº ÀÛ¿ëÀÌ °¨¼ÒÇÏ¿© ¹ß»ýÇÏ¸ç ºñÁ¤»óÀûÀ¸·Î ¸¹Àº ¾çÀÇ Èñ¼®µÈ ¼Òº¯ÀÌ Æ¯Â¡ÀÌ´Ù.
24hr urine volume > 50 mL/kg, U-osmolality < 300 mmol/kg
polyuria, urinary frequency, enuresis and/or nocturia, ÀÌ·Î ÀÎÇÑ sleep disturbance, mild
daytime fatigue or somnolence°¡ »ý±ä´Ù. polydipsia¸¦ ÅëÇØ º¸»óµÇ¹Ç·Î dehydration sign
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1) deficient secretion : primary or secondary

(1) primary deficiency: agenesis or irreversible destruction of the neurohypophysis
= neurohypophyseal DI, neurogenic DI, pituitary DI, cranial DI, or central DI
congenital, acquired, or genetic disorder¿¡ ¹ß»ýÇÏÁö¸¸ ¹ÝÁ¤µµ´Â idiopathic.
¨ç genetic form : ÈçÈ÷ autosomal dominant mode & diverse mutation
(AVP-neurophysin II gene)
Çб³Á¤º¸ 2ÁÖ°£ ´Ù¿î¹ÞÀº ÇлýÀÇ Çб³Á¤º¸¸¦ º¸¿©ÁÝ´Ï´Ù.(5P ¼Ò¿ä)
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À§ Á¤º¸ ¹× °Ô½Ã¹° ³»¿ëÀÇ ºÒ¹ýÀû ÀÌ¿ë, ¹«´Ü ÀüÀ硤¹èÆ÷´Â ±ÝÁöµÇ¾î ÀÖ½À´Ï´Ù.ÀúÀÛ±ÇÄ§ÇØ, ¸í¿¹ÈÑ¼Õ µî ºÐÀï¿ä¼Ò ¹ß°ß½Ã °í°´¼¾ÅÍÀÇ ÀúÀÛ±ÇÄ§ÇØ ½Å°í¼¾Å͸¦ ÀÌ¿ëÇØ Áֽñ⠹ٶø´Ï´Ù.

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